PEX7 Rabbit Polyclonal Antibody
No Size Price Availability  
ARP5191-61 50ul 1500.00 In Stock
ARP5191-61 100ul 2000.00 In Stock
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Source: Rabbit Gene Id: 5191
Isotype: IgG Swiss Prot: O00628
purity: Affinity purification
Background:
This gene encodes the cytosolic receptor for the set of peroxisomal matrix enzymes targeted to the organelle by the peroxisome targeting signal 2 (PTS2). Defects in this gene cause peroxisome biogenesis disorders (PBDs), which are characterized by multiple defects in peroxisome function. There are at least 14 complementation groups for PBDs, with more than one phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene have been associated with PBD complementation group 11 (PBD-CG11) disorders, rhizomelic chondrodysplasia punctata type 1 (RCDP1), and Refsum disease (RD). [provided by RefSeq
Reactivity Human, Mouse, Rat
Tested applications WB IHC
Clonality Polyclonal Antibody
Calculated MW 40 kDa
Recommended Dilutions
WB 1:500-1:1000
IHC 1:50-1:200
Immunogen A synthetic peptide
Storage Store at -20°C or -80°C in PBS with 0.02% sodium azide and 50% glycerol. Avoid freeze/thaw cycles.
Synonym Peroxisomal targeting signal 2 receptor,PTS2 receptor, Peroxin-7
This product is for research use only, not for diagnostic or therapeutic use!

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