Species: | Rabbit |
Applications: | WB IHC IF |
Immunogen Range: | KLH conjugated synthetic peptide derived from human ACOX1 |
Clonality: | Polyclonal Antibody |
Isotype: | IgG |
GENE ID: | 51 |
Swiss Prot: | |
Synonyms: | ACOX1, ACOX1_HUMAN, AOX antibody Palmitoyl CoA oxidase, Palmitoyl-CoA oxidase, Peroxisomal acyl coenzyme A oxidase 1, Peroxisomal acyl-coenzyme A oxidase 1, SCOX, Straight chain acyl CoA oxidase, Straight-chain acyl-CoA oxidase. |
Purification: | Purified by Protein A. |
Storage: | Aqueous buffered solution containing 100ug/ml BSA, 50% glycerol and 0.09% sodium azide. Store at -20℃ for 12 months |
Background: | Defects in ACOX1 are the cause of adrenoleukodystrophy pseudoneonatal (Pseudo-NALD); also known as peroxisomal acyl-CoA oxidase deficiency. Pseudo-NALD is a peroxisomal single-enzyme disorder. Clinical features include mental retardation, leukodystrophy, seizures, mild hepatomegaly, hearing deficit. Pseudo-NALD is characterized by increased plasma levels of very-long chain fatty cids, due to decreased or absent peroxisome acyl-CoA oxidase activity. Peroxisomes are intact and functioning. |
Caculated MW: | / |
Observed MW: | Refer to Figures |
Applications: |
WB 1:100-1:1000 IHC 1:100-1:500 IF 1:50-1:200 |
Reacitivity: | Human, Mouse, Rat |