Species: | Rabbit |
Applications: | WB IHC IF |
Immunogen Range: | A recombinant protein of human EHHADH |
Clonality: | Polyclonal Antibody |
Isotype: | IgG |
GENE ID: | 1962 |
Swiss Prot: | Q08426 |
Synonyms: | LBP, ECHD, LBFP, PBFE, FRTS3, L-PBE |
Purification: | Affinity purification |
Storage: | Store at -20oC (regular) or -80oC (long term). Avoid freeze / thaw cycles. Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3. |
Background: | The protein encoded by this gene is a bifunctional enzyme and is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of the encoded protein contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in this gene are a cause of peroxisomal disorders such as Zellweger syndrome. Two transcript variants encoding different isoforms have been found for this gene. |
Caculated MW: | 79kDa |
Observed MW: | Refer to Figures |
Applications: |
WB 1:500 - 1:2000 IHC 1:50 - 1:200 IF 1:50- 1:100 |
Reacitivity: | Human |